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Pediatric Surgery International

Published in:

01-08-2012 | Original Article

Postoperative complications in adults with anorectal malformation: a need for transition. German Network for Congenital Uro-REctal Malformations (CURE-Net)

Authors: Dominik Schmidt, Ekkehart Jenetzky, Nadine Zwink, Eberhard Schmiedeke, Stefanie Maerzheuser

Published in: Pediatric Surgery International | Issue 8/2012

Abstract

Purpose

The aim of the German Network for Congenital Uro-REctal malformations (CURE-Net) is to collect data of affected patients with anorectal malformation (ARM) to investigate molecular causes, clinical implications and psychosocial outcome. The current issue was to examine the transition to adulthood in adults with ARM and to explore condition-related needs and skills required.

Methods

This qualitative study is part of a larger multi-center study of clinical queries and quality of life in patients with ARM. The guided interview focused on the analysis of medical data and personal questionnaires.

Results

Interviews were completed with 55 (23 females, 32 males) participants, age ranging from 18 to 56 years. Twenty-one patients suffered from mucosal prolapse, 18 patients had had megasigmoid/megacolon. Relevant stenosis of the neo-anus occurred in 13 (42 %) males and 4 (18 %) females, permanent neurogenic bladder dysfunction in 10 (32 %) males and 4 (18 %) females, recurrent urinary tract infections in 10 (32 %) males and 13 (59 %) females, latex allergy in 10 (32 %) males and 7 (32 %) females. Thirty-seven (70 %) patients had to be reoperated. Forty-one (75 %) patients needed means of aftercare to achieve social continence.

Conclusion

The study wants to contribute to a better understanding of the challenges of transition for adults with ARM.

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Title: Postoperative complications in adults with anorectal malformation: a need for transition. German Network for Congenital Uro-REctal Malformations (CURE-Net)
Authors: Dominik Schmidt
Ekkehart Jenetzky
Nadine Zwink
Eberhard Schmiedeke
Stefanie Maerzheuser
Publication date: 01-08-2012
Publisher: Springer-Verlag
Published in: Pediatric Surgery International / Issue 8/2012
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-012-3120-8

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Postoperative complications in adults with anorectal malformation: a need for transition. German Network for Congenital Uro-REctal Malformations (CURE-Net)

Abstract

Purpose

Methods

Results

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Purpose

Methods

Results

Conclusion

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