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Published in: Orphanet Journal of Rare Diseases 1/2024

Open Access 01-12-2024 | Pneumothorax | Letter to the Editor

Intraoperative mechanical ventilation and incidence of pneumothorax in lymphangioleiomyomatosis

Authors: Chen Sun, Lijian Pei, Chongsheng Cheng, Bing Bai, Kai-Feng Xu, Yuguang Huang

Published in: Orphanet Journal of Rare Diseases | Issue 1/2024

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Abstract

Patients with lymphangioleiomyomatosis (LAM) are considered high risk for most surgeries and require specific anesthetic considerations mainly because of the common spontaneous pneumothorax (PTX). To explore whether intraoperative mechanical ventilation could increase the risk of PTX in those patients, we included 12 surgical patients with LAM in this study, of whom four (33.3%) experienced postoperative PTX. According to our results, patients with higher CT grade, poorer pulmonary function, and a history of preoperative PTX might be more likely to develop postoperative PTX. However, intraoperative mechanical ventilation did not show obvious influence, which might help clinicians reconsider the perioperative management of LAM patients.
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Metadata
Title
Intraoperative mechanical ventilation and incidence of pneumothorax in lymphangioleiomyomatosis
Authors
Chen Sun
Lijian Pei
Chongsheng Cheng
Bing Bai
Kai-Feng Xu
Yuguang Huang
Publication date
01-12-2024
Publisher
BioMed Central
Published in
Orphanet Journal of Rare Diseases / Issue 1/2024
Electronic ISSN: 1750-1172
DOI
https://doi.org/10.1186/s13023-024-03117-w

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