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01-07-2012 | Case Report

Perianal rhabdomyosarcoma presenting 21 months after hamartoma excision

Authors: N. Piché, N. Patey, D. Dal Soglio, Y. Samson, S. Bouchard

Published in: Pediatric Surgery International | Issue 7/2012

Abstract

Perianal rhabdomyosarcoma is a rare type of tumor with a relatively poor prognosis. We present the case of a patient who presented with a cutaneous perianal hamartoma at the age of 6 weeks. 21 months latter a recurrent mass at the excision site proved to be an embryonal rhabdomyosarcoma involving the anal sphincter. A pathologic review of the two specimens confirmed their relatedness. This report highlights the need to maintain a high level of suspicion in cases of recurrence following excision of a benign lesion.

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Title: Perianal rhabdomyosarcoma presenting 21 months after hamartoma excision
Authors: N. Piché
N. Patey
D. Dal Soglio
Y. Samson
S. Bouchard
Publication date: 01-07-2012
Publisher: Springer-Verlag
Published in: Pediatric Surgery International / Issue 7/2012
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-012-3074-x

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Perianal rhabdomyosarcoma presenting 21 months after hamartoma excision

Abstract

Keynote webinar | Spotlight on medication adherence

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Abstract

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