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Indian Journal of Thoracic and Cardiovascular Surgery

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01-09-2017 | Case report

Pentalogy and Cantrell and sternal cleft: a report of two cases and review of literature

Authors: Josephat Maduabuchi Chinawa, Vijay Agarwal, Swati Garekar, Sarang Gaikwad, Bhadra Trivedi

Published in: Indian Journal of Thoracic and Cardiovascular Surgery | Issue 3/2017

Abstract

Pentalogy of Cantrell refers to a clinical entity seen in children, with attendant impact on quality of life, if early intervention is not given. We report two cases who presented to our hospital, Fortis hospital Mulund, Mumbai. The first had a sternal cleft with partial ectopia thoracic while the second case had a type 3 Pentalogy of Cantrell. Computerized axial tomography (CT scan) confirmed the diagnosis. Both had surgical repair with a very good outcome.

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Kumar B, Sharma C, Sinha DD, Sumanlata. Ectopia cordis associated with Cantrell’s pentalogy. Ann Thorac Med. 2008;3:152–3.CrossRefPubMedPubMedCentral

Lopez JA, Lopez AG, Leon IH. Presentation and discussion of a patient with pentalogy of Cantrell. Cuban Rev Obstet Ginecol. 2004;30:2.

Skandalakis JE, Gray SW, Ricketts R, Skandalakis LJ. The anterior body wall. In: Skandalakis JE, Gray SW, editors. Embryology for surgeons. 2nd ed. Baltimore: Williams and Wilkins; 1994. p. 552–9.

Herman TE, Siegel MJ. Cantrell syndrome. J Perinatol. 2010;30:298–9.CrossRefPubMed

Paulo RS, Sónia A, Alexandra C, Gonçalo CS, Luis GL, Manuel PM. Congenital medium sternal cleft with partial ectopia cordis repair. BMJ Case Rep. 2009;2009. doi:10.1136/bcr.06.2009.2018.

Patil AR, Praveen LS, Ambica V. Pentalogy of Cantrell: a case report. BJRI case reports. 2015;1:1–4. doi:10.1259/bjrcr.20140002.

Rubens-Figuero AJ, Sosa-Cruz EF, Diaz Garcia L, Carrasco-Daza D. Cardiac malformations in patients with Pentalogy of Cantrell and ectopia cordis. Rev Esp Cardiol. 2011;64:615–618.

Sowande OA, Anyanwu LJ, Taliban AO, Babalola OR, Adejuyigbe O. Pentalogy of Cantrell: a report of three cases. J Surg Tech Case Rep. 2010;2:20–3.CrossRefPubMedPubMedCentral

O'Gorman CS, Tortoriello TA, McMahon CJ. Outcome of children with Pentalogy of Cantrell following cardiac surgery. Pediatr Cardiol. 2009;30:426–30.CrossRefPubMed

Title: Pentalogy and Cantrell and sternal cleft: a report of two cases and review of literature
Authors: Josephat Maduabuchi Chinawa
Vijay Agarwal
Swati Garekar
Sarang Gaikwad
Bhadra Trivedi
Publication date: 01-09-2017
Publisher: Springer Singapore
Published in: Indian Journal of Thoracic and Cardiovascular Surgery / Issue 3/2017
Print ISSN: 0970-9134
Electronic ISSN: 0973-7723
DOI: https://doi.org/10.1007/s12055-017-0525-y

At a glance: The STEP trials

Springer Medicine

Pentalogy and Cantrell and sternal cleft: a report of two cases and review of literature

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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