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01-09-2021 | Paget's Disease of Bone | Original Article

Impact of Surgery on Extramammary Paget’s Disease Vulva: a Case Series

Authors: J. S. Anjana, P. Rema, S. Suchetha, J. Siva Ranjith, Amrita B. Rao, T. R. Preethi

Published in: Indian Journal of Surgical Oncology | Issue 3/2021

Abstract

Extramammary Paget’s disease is a rare neoplasm that may affect the vulva. It usually presents as a pruritic red eczematous lesion with islands of hyperkeratosis that is often mistaken for other benign conditions. There are no specific guidelines for the management of this disease. Surgical excision is the standard treatment but recurrences are common in spite of extensive surgery with negative margins. We report here a series of 7 cases of Paget’s disease vulva treated by primary surgery. The series highlights some of the challenges in the diagnosis and management of Paget’s disease vulva.

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Title: Impact of Surgery on Extramammary Paget’s Disease Vulva: a Case Series
Authors: J. S. Anjana
P. Rema
S. Suchetha
J. Siva Ranjith
Amrita B. Rao
T. R. Preethi
Publication date: 01-09-2021
Publisher: Springer India
Keyword: Paget's Disease of Bone
Published in: Indian Journal of Surgical Oncology / Issue 3/2021
Print ISSN: 0975-7651
Electronic ISSN: 0976-6952
DOI: https://doi.org/10.1007/s13193-021-01366-w

At a glance: The STEP trials

Springer Medicine

Impact of Surgery on Extramammary Paget’s Disease Vulva: a Case Series

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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