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01-07-2015 | Case Report

Orbital lymphomatoid granulomatosis – a rare cause of proptosis

Authors: Jacqueline du Toit, Tracy Kilborn, Ann Van Eyssen, Komala Pillay

Published in: Pediatric Radiology | Issue 7/2015

Abstract

A 1-year-old girl with unilateral proptosis was found to have primary orbital lymphomatoid granulomatosis – a condition rarely occurring in children. This multisystem angiocentric, angiodestructive, lymphoproliferative disease typically involves the lungs, with ocular involvement being extremely uncommon. Our case serves to illustrate the imaging findings of this unusual condition and highlight a rare cause of proptosis.

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Title: Orbital lymphomatoid granulomatosis – a rare cause of proptosis
Authors: Jacqueline du Toit
Tracy Kilborn
Ann Van Eyssen
Komala Pillay
Publication date: 01-07-2015
Publisher: Springer Berlin Heidelberg
Published in: Pediatric Radiology / Issue 7/2015
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-014-3206-7

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Orbital lymphomatoid granulomatosis – a rare cause of proptosis

Abstract

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Abstract

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