Published in:
24-06-2023 | Neurofibromatosis Type 1 | Case Report
Kaposiform hemangioendothelioma of skull base with dura invasion in a pediatric patient: a case report
Authors:
Seong-Chan Jung, Tae-Young Jung, Tae-Kyu Lee, Yeong Jin Kim, Hee Jo Baek, Sung Soon Kim
Published in:
Child's Nervous System
|
Issue 11/2023
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Abstract
Kaposiform hemangioendothelioma is an extremely rare vascular tumor which shows aggressive local growth. We present a case of rapid growing vascular skull tumor with dura invasion in a pediatric patient with neurofibromatosis type 1. A 14-year-old male complained of headache and dizziness for 1 month after minor head trauma. Brain magnetic resonance imaging (MRI) revealed a 5-cm-sized tumor in the left frontotemporal bone with internal hemorrhage and cystic changes. The gross total resection of tumor was done. At the 7-month follow-up, brain MRI revealed a recurrent skull tumor with intracranial dura mass. He underwent second surgery, and the pathologic diagnosis was suggestive of Kaposiform hemangioendothelioma. For this vascular proliferative tumor, mTOR inhibitor was treated for 6 months, and there was the recurred nodular-enhancing mass along the sphenoid ridge. After additional 2 months of medication, the following MRI revealed a decreased nodular-enhancing mass.