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Open Access 01-12-2024 | Neurofibromatosis Type 1 | Case report

Robotic resection for splenic artery aneurysm associated with neurofibromatosis type 1: a case report

Authors: Akihiko Ueda, Kenta Saito, Hiromichi Murase, Tomokatsu Kato, Hiroyuki Imafuji, Mamoru Morimoto, Ryo Ogawa, Hiroki Takahashi, Yoichi Matsuo, Shuji Takiguchi

Published in: Journal of Medical Case Reports | Issue 1/2024

Abstract

Background

Neurofibromatosis type 1 is an autosomal-dominant disease characterized by café-au-lait spots and neurofibromas, as well as various other symptoms in the bones, eyes, and nervous system. Due to its connection with vascular fragility, neurofibromatosis type 1 has been reported to be associated with vascular lesions, such as aneurysms. However, there have been few reports of abdominal visceral aneurysms associated with neurofibromatosis type 1. Furthermore, there have been no reports of robotic treatment of aneurysms associated with neurofibromatosis type 1. In this report, we describe the case of a patient with neurofibromatosis type 1 with a splenic artery aneurysm who was successfully treated with robotic surgery.

Case presentation

This report describes a 41-year-old Asian woman with a history of neurofibromatosis type 1 who was referred to our hospital for evaluation of a 28 mm splenic artery aneurysm observed on abdominal ultrasound. The aneurysm was in the splenic hilum, and transcatheter arterial embolization was attempted; however, this was difficult due to the tortuosity of the splenic artery. Thus, we suggested minimally invasive robotic surgery for treatment and resection of the splenic artery aneurysm with preservation of the spleen. The postoperative course was uneventful, and the patient was discharged on the eighth day after surgery. At 1 year of follow-up, the patient was doing well, with no evidence of recurrence.

Conclusion

We encountered a rare case of splenic artery aneurysm in a patient with neurofibromatosis type 1 who was successfully treated with robotic surgery. There is no consensus on treatment modalities for neurofibromatosis-related aneurysms, and endovascular treatment is considered safe and effective; however, surgery remains an important treatment modality. Especially in patients with stable hemodynamic status, robotic surgery may be considered as definitive treatment. To our knowledge, this is the first successfully treated case of a splenic artery aneurysm in a patient with neurofibromatosis type 1.

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Title: Robotic resection for splenic artery aneurysm associated with neurofibromatosis type 1: a case report
Authors: Akihiko Ueda
Kenta Saito
Hiromichi Murase
Tomokatsu Kato
Hiroyuki Imafuji
Mamoru Morimoto
Ryo Ogawa
Hiroki Takahashi
Yoichi Matsuo
Shuji Takiguchi
Publication date: 01-12-2024
Publisher: BioMed Central
Keywords: Neurofibromatosis Type 1
Aneurysm
Aneurysm
Laparotomy
Laparotomy
Published in: Journal of Medical Case Reports / Issue 1/2024
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/s13256-024-04440-3

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Robotic resection for splenic artery aneurysm associated with neurofibromatosis type 1: a case report

Abstract

Background

Case presentation

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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