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Published in: BMC Urology 1/2022

Open Access 01-12-2022 | Nephrectomy | Case report

Successful management of ectopic kidney stones in a patient with situs inversus totalis: a rare case report

Authors: Marah Mansour, Abdulmonem Naksho, Yassamine Ouerdane, Tamim Alsuliman, Hani Almozawer, Khaled Alrebdawi

Published in: BMC Urology | Issue 1/2022

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Abstract

Background

Situs inversus totalis is a very rare congenital anatomical variation, in which all thoracic and abdominal organs are right-left inverted. This condition is associated with an increased risk of organ malformations including ectopic kidney, which is a very rare combination.

Case presentation

A 56-year-old male presented with colicky left iliac pain associated with nausea, vomiting, and irritative lower urinary symptoms. The patient has a medical history of recurrent lower urinary infections and a family history of situs inversus totalis. Radiological images demonstrated dextrocardia, situs inversus totalis of all the abdominal organs, and an ectopic pelvic kidney on the left side, with 4 stones inside it. Left nephrectomy was performed due to extensive renal damage. At discharge and during follow-up, the patient's condition was satisfactory and stable.

Conclusions

The ectopic kidney may present diagnostic and therapeutic challenges when associated with situs inversus.
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Metadata
Title
Successful management of ectopic kidney stones in a patient with situs inversus totalis: a rare case report
Authors
Marah Mansour
Abdulmonem Naksho
Yassamine Ouerdane
Tamim Alsuliman
Hani Almozawer
Khaled Alrebdawi
Publication date
01-12-2022
Publisher
BioMed Central
Published in
BMC Urology / Issue 1/2022
Electronic ISSN: 1471-2490
DOI
https://doi.org/10.1186/s12894-022-01137-x

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