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Published in: Journal of Neuro-Oncology 2/2007

01-09-2007 | Imagers in Neuron-oncology clinical-patient studies

MRI of primary spinal atypical teratoid/rhabdoid tumor: a case report and literature review

Authors: Hiroshi Kodama, Masayuki Maeda, Hiroshi Imai, Toshio Matsubara, Waro Taki, Kan Takeda

Published in: Journal of Neuro-Oncology | Issue 2/2007

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Abstract

Primary spinal atypical teratoid/rhabdoid tumor (AT/RT) is extremely rare. A 9-month-old boy presented with tetraparesis. Subsequent MRI showed an intradural extramedullary bulky mass extending from C4 to T6. Subtotal removal of the tumor was performed and spinal AT/RT was proven histologically. Despite chemotherapy and radiation therapy, leptomeningeal dissemination was found on follow-up MRI. The patient died 20 months after his initial symptoms. We describe the MRI findings of this case and review the literature describing this rare disease.
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Metadata
Title
MRI of primary spinal atypical teratoid/rhabdoid tumor: a case report and literature review
Authors
Hiroshi Kodama
Masayuki Maeda
Hiroshi Imai
Toshio Matsubara
Waro Taki
Kan Takeda
Publication date
01-09-2007
Published in
Journal of Neuro-Oncology / Issue 2/2007
Print ISSN: 0167-594X
Electronic ISSN: 1573-7373
DOI
https://doi.org/10.1007/s11060-007-9359-6

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