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Diagnostic Pathology
Published in: Diagnostic Pathology 1/2010

Open Access 01-12-2010 | Case Report

Malignant peripheral nerve sheath tumor associated with neurofibromatosis type 1, with metastasis to the heart: a case report

Authors: Masanori Kitamura, Naoki Wada, Shigenori Nagata, Norishige Iizuka, Yu-Fen Jin, Miki Tomoeda, Michiko Yuki, Norifumi Naka, Nobuhito Araki, Chikao Yutani, Yasuhiko Tomita

Published in: Diagnostic Pathology | Issue 1/2010

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Abstract

A rare case is presented of a 61-year-old man with a malignant peripheral nerve sheath tumor associated with neurofibromatosis type 1, with metastasis to the heart. The primary tumor originated in the right thigh in 1982. Since then, the patient has had repeated local recurrences in spite of repeated surgical treatment and adjuvant chemotherapy. He has developed previous metastases of the lung and heart. The patient died of cardiac involvement.
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Metadata
Title
Malignant peripheral nerve sheath tumor associated with neurofibromatosis type 1, with metastasis to the heart: a case report
Authors
Masanori Kitamura
Naoki Wada
Shigenori Nagata
Norishige Iizuka
Yu-Fen Jin
Miki Tomoeda
Michiko Yuki
Norifumi Naka
Nobuhito Araki
Chikao Yutani
Yasuhiko Tomita
Publication date
01-12-2010
Publisher
BioMed Central
Published in
Diagnostic Pathology / Issue 1/2010
Electronic ISSN: 1746-1596
DOI
https://doi.org/10.1186/1746-1596-5-2

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