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01-08-2003 | Case Report

Long segment Hirschsprung's disease in the Waardenburg-Shah syndrome

Authors: E. J. Gnananayagam, R. Solomon, A. Chandran, S. Anbarasi, S. Sen, P. D. Moses

Published in: Pediatric Surgery International | Issue 6/2003

Abstract.

Presentation with signs of bowel obstruction in an infant with Waardenburg syndrome should raise the suspicion of aganglionosis. We report such a case of long segment Hirschsprung's disease associated with Waardenburg syndrome. Long term care of such children is fraught with high morbidity and mortality.

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Title: Long segment Hirschsprung's disease in the Waardenburg-Shah syndrome
Authors: E. J. Gnananayagam
R. Solomon
A. Chandran
S. Anbarasi
S. Sen
P. D. Moses
Publication date: 01-08-2003
Publisher: Springer-Verlag
Published in: Pediatric Surgery International / Issue 6/2003
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-002-0944-7

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Long segment Hirschsprung's disease in the Waardenburg-Shah syndrome

Abstract.

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract.

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