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Skeletal Radiology
Published in: Skeletal Radiology 6/2008

01-06-2008 | Case Report

Lipofibromatosis: report of a rare paediatric soft tissue tumour

Authors: A. N. Deepti, Vrisha Madhuri, Noel Malcolm Walter, Rekha Aley Cherian

Published in: Skeletal Radiology | Issue 6/2008

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Abstract

The clinical, radiological and pathological features of a case of lipofibromatosis, a rare paediatric soft tissue neoplasm, are described. The tumour involved the foot of a male infant and was present at birth. Magnetic resonance imaging showed a lipomatous mass, with splaying of muscles of the sole by lobules of fat. Histopathological examination revealed typical findings of an admixture of mature adipose tissue and fibroblastic elements. The radiological and pathological features helpful in differentiating this entity from other fibro-fatty paediatric soft tissue tumours is discussed, and the relevant literature is briefly reviewed.
Literature
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Fetsch JF, Miettinen M, Laskin WB, Michal M, Enzinger FM. A clinicopathologic study of 45 pediatric soft tissue tumours with an admixture of adipose tissue and fibroblastic elements and a proposal for classification as lipofibromatosis. Am J Surg Pathol 2000; 24: 1491–1500.PubMedCrossRef
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Miettinen M, Fetsch JF. Lipofibromatosis. In: Fletcher CDM, Unni KK, Mertens F, eds. WHO classification of tumours. Pathology and genetics of tumours of soft tissue and bone. Lyon: IARC Press; 2002: 85.
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Metadata
Title
Lipofibromatosis: report of a rare paediatric soft tissue tumour
Authors
A. N. Deepti
Vrisha Madhuri
Noel Malcolm Walter
Rekha Aley Cherian
Publication date
01-06-2008
Publisher
Springer-Verlag
Published in
Skeletal Radiology / Issue 6/2008
Print ISSN: 0364-2348
Electronic ISSN: 1432-2161
DOI
https://doi.org/10.1007/s00256-008-0458-z

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