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Clinical Sarcoma Research

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Open Access 01-12-2017 | Case report

Two years survival of primary cardiac leiomyosarcoma managed by surgical and adjuvant therapy

Authors: K. Behi, M. Ayadi, E. Mezni, K. Meddeb, A. Mokrani, Y. Yahyaoui, F. Ksontini, H. Rais, N. Chrait, A. Mezlini

Published in: Clinical Sarcoma Research | Issue 1/2017

Abstract

Background

Cardiac tumors are a very rare entity. Leiomyosarcoma represents less than 1% of cases.

Case presentation

a 51-year-old woman diagnosed with primary left atrium leiomyosarcoma. She was treated by optimal surgery and adjuvant chemotherapy. She is still alive after a follow-up of 24 months without evidence of local or distant recurrence.

Conclusions

Cardiac leiomyosarcoma is a rare tumor with a dismal prognosis. Surgery is the mainstay of treatment. Adjuvant treatment is still controversial.

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Title: Two years survival of primary cardiac leiomyosarcoma managed by surgical and adjuvant therapy
Authors: K. Behi
M. Ayadi
E. Mezni
K. Meddeb
A. Mokrani
Y. Yahyaoui
F. Ksontini
H. Rais
N. Chrait
A. Mezlini
Publication date: 01-12-2017
Publisher: BioMed Central
Published in: Clinical Sarcoma Research / Issue 1/2017
Electronic ISSN: 2045-3329
DOI: https://doi.org/10.1186/s13569-017-0069-3

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