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Clinical Sarcoma Research
Published in: Clinical Sarcoma Research 1/2016

Open Access 01-12-2016 | Case Report

Primary Kaposi’s sarcoma of the nasal cavity: a case report and review of the literature

Authors: Karima Mouden, Mouna Khmou, Saida Loughmari, Afaf Semmar, Hanan El Kacemi, Basma El Khannoussi, Tayeb Kebdani, Sanaa Elmajjaoui, Noureddine Benjaafar

Published in: Clinical Sarcoma Research | Issue 1/2016

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Abstract

Background

Kaposi sarcoma is a neoplastic vascular disorder. It usually present on the skin of the upper and lower extremities, rarely in the mucosa of the head and neck. The most common sites reported are within the oral cavity, particularly on the palate. Other mucosal sites are rare. We present an unusual case where the primary manifestation of the Kaposi’s sarcoma was in the nasal mucosa.

Case presentation

A 56-year-old female of Mediterranean descent presented with a 1 year history of swelling on the left side of her nose, nasal obstruction and occasional minor epistaxes. Physical examination showed a firm and bulging polypoid mass which filled the left nasal cavity without cutaneous lesions.
Computed tomography (CT) demonstrated a tumor, measuring 77 mm in diameter, occupying the left nasal cavity causing erosion of nasal septum and extending posteriorly to the left choana and nasopharynx. There was bilateral cervical lymphadenopathy. Patient treated with chemotherapy alone. She was in a complete response after the first cycle. The patient received no further treatment. She needs a regular medical checkups that include a review of a patient’s medical history and a complete physical exam. She is in excellent local control over 12 months.

Conclusions

A review of the literature revealed that only seven cases of primary Kaposi sarcoma of the nasal cavity have previously been published and only two of them presented in a patient not associated with the acquired immunodeficiency syndrome. Here, we report the third case where the primary manifestation of the Kaposi sarcoma was in the nasal cavity in a patient with an adequate immune system.
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Metadata
Title
Primary Kaposi’s sarcoma of the nasal cavity: a case report and review of the literature
Authors
Karima Mouden
Mouna Khmou
Saida Loughmari
Afaf Semmar
Hanan El Kacemi
Basma El Khannoussi
Tayeb Kebdani
Sanaa Elmajjaoui
Noureddine Benjaafar
Publication date
01-12-2016
Publisher
BioMed Central
Published in
Clinical Sarcoma Research / Issue 1/2016
Electronic ISSN: 2045-3329
DOI
https://doi.org/10.1186/s13569-016-0044-4

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