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Open Access 01-12-2023 | Ewing's Sarcoma | Case report

Primary adrenal Ewing’s sarcoma family of tumors with tumor thrombus of the inferior vena cava: a case report

Authors: Kaya Atagi, Takashi Karashima, Keisuke Mizutani, Hideo Fukuhara, Satoshi Fukata, Yujiro Miura, Atsuyuki Mitsuishi, Kazuhiro Hanazaki, Sunao Uemura, Ryohei Miyazaki, Takashi Anayama, Mayuka Yamane, Mizu Sakai, Mitsuko Iguchi, Kenji Yorita, Keiji Inoue

Published in: Journal of Medical Case Reports | Issue 1/2023

Abstract

Background

Ewing’s sarcoma is a malignant neoplasm that mainly occurs in skeletal tissue but can rarely arise in soft tissues. Recently, small round cell tumors (including Ewing’s sarcoma) caused by chromosomal translocations have been collectively termed Ewing’s sarcoma family of tumors. We report a rare case of primary adrenal Ewing’s sarcoma family of tumors with tumor thrombus.

Case presentation

A 22-year-old Asian woman was referred to our hospital with a left retroperitoneal tumor 19 cm in diameter. Tumor thrombus was identified from the left adrenal vein to the inferior vena cava, infiltrating the right atrium. Total tumor excision with left adrenalectomy, nephrectomy, and thrombectomy was performed under hypothermic circulatory arrest, followed by seven courses of adjuvant chemotherapy. The patient has shown no signs of recurrence as of 26 months postoperatively.

Conclusion

Radical surgery combined with systemic chemotherapy may contribute to good prognosis in patients with primary adrenal Ewing’s sarcoma family of tumors.

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Title: Primary adrenal Ewing’s sarcoma family of tumors with tumor thrombus of the inferior vena cava: a case report
Authors: Kaya Atagi
Takashi Karashima
Keisuke Mizutani
Hideo Fukuhara
Satoshi Fukata
Yujiro Miura
Atsuyuki Mitsuishi
Kazuhiro Hanazaki
Sunao Uemura
Ryohei Miyazaki
Takashi Anayama
Mayuka Yamane
Mizu Sakai
Mitsuko Iguchi
Kenji Yorita
Keiji Inoue
Publication date: 01-12-2023
Publisher: BioMed Central
Keywords: Ewing's Sarcoma
Fluorescence in Situ Hybridization
Adrenalectomy
Ewing's sarcoma
Adrenalectomy
Thrombectomy
Cytostatic Therapy
Published in: Journal of Medical Case Reports / Issue 1/2023
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/s13256-023-03837-w

ACC 2024 Congress

Springer Medicine

Primary adrenal Ewing’s sarcoma family of tumors with tumor thrombus of the inferior vena cava: a case report

Abstract

Background

Case presentation

Conclusion

ACC 2024 Congress

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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