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Published in: Journal of Medical Case Reports 1/2018

Open Access 01-12-2018 | Case report

Surgical outcome of jejunum-jejunum intussusception secondary to Rapunzel syndrome: a case report

Authors: Martín Adrián Bolívar-Rodríguez, Rodolfo Fierro-López, Adrián Pamanes-Lozano, Marcel Antonio Cazarez-Aguilar, Benny Alonso Osuna-Wong, José Cándido Ortiz-Bojórquez

Published in: Journal of Medical Case Reports | Issue 1/2018

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Abstract

Background

Adult intestinal intussusception is a rare condition caused by the mechanical disruption of bowel motility. A bezoar is defined as indigestible material inside the gastrointestinal tract that develops into a trapped mass; the most frequent bezoar is a trichobezoar. When a trichobezoar extends into the small intestine it is defined as Rapunzel’s syndrome. Literature describing complications related to this pathology remains scarce.

Case presentation

A 16-year-old Mexican girl presented to our emergency room with acute abdomen and a presumptive diagnosis of intestinal obstruction. Computed tomography was suggestive of intussusception. Surgery confirmed a jejunal-jejunal intussusception with a mass within the gastric cavity extending into her small intestine, corresponding to a trichobezoar. A manual intussusception reduction and a gastrotomy with extraction of the trichobezoar were performed.

Conclusions

We present a case of a jejunum intussusception as a complication of Rapunzel syndrome. Our patient had a favorable outcome after surgical intervention with a manual intussusception reduction, with retrograde displacement of the trichobezoar into the gastric lumen, and a complete extraction through a gastrostomy. Follow-up included psychiatric evaluation.
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Metadata
Title
Surgical outcome of jejunum-jejunum intussusception secondary to Rapunzel syndrome: a case report
Authors
Martín Adrián Bolívar-Rodríguez
Rodolfo Fierro-López
Adrián Pamanes-Lozano
Marcel Antonio Cazarez-Aguilar
Benny Alonso Osuna-Wong
José Cándido Ortiz-Bojórquez
Publication date
01-12-2018
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2018
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/s13256-018-1883-9

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