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Published in: Journal of Medical Case Reports 1/2017

Open Access 01-12-2017 | Case report

Giant mucinous adenocarcinoma of the appendix: a case report

Authors: Sheng-Chun Dang, Ming-Ming Sun, Lu-Lu Liu, Abdul Malik, Jian-Xin Zhang, Yi-Yi Fan, Song Zou, Lei Cui, Jian-Guo Qu, Ji-Xiang Chen

Published in: Journal of Medical Case Reports | Issue 1/2017

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Abstract

Background

Appendiceal mucinous adenocarcinoma is an extremely rare disease in clinical practice. Here, we report a case of unprecedented size that occupied the entire abdomen of a man.

Case presentation

A 49-year-old Chinese Han man presented with symptoms of abdominal distension. During a computed tomography imaging examination, a cystic-solid mass that occupied his entire abdominal cavity was detected. During exploratory laparotomy, an appendiceal tumor in his abdominal-pelvic cavity measuring 27.6 × 14.2 cm was found, and he underwent tumor resection. The pathology of the tumor identified a well-differentiated appendiceal mucinous adenocarcinoma with mucin infiltrating into the soft tissue of the lump edge and omentum tissue. After surgery, our patient accepted intraperitoneal infusion chemotherapy. At present, he has had no recurrence for 15 months.

Conclusions

To the best of our knowledge, the present case is the largest appendiceal mucinous adenocarcinoma reported. Surgical tumor resection is the preferred treatment for appendiceal mucinous adenocarcinoma. This is supplemented by chemotherapy which can further prolong survival.
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Metadata
Title
Giant mucinous adenocarcinoma of the appendix: a case report
Authors
Sheng-Chun Dang
Ming-Ming Sun
Lu-Lu Liu
Abdul Malik
Jian-Xin Zhang
Yi-Yi Fan
Song Zou
Lei Cui
Jian-Guo Qu
Ji-Xiang Chen
Publication date
01-12-2017
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2017
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/s13256-017-1385-1

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