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Journal of Cardiothoracic Surgery
Published in: Journal of Cardiothoracic Surgery 1/2017

Open Access 01-12-2017 | Case report

Doege-potter syndrome: a report of a histologically benign but clinically malignant case

Authors: Do Wan Kim, Kook Joo Na, Ju Sik Yun, Sang Yun Song

Published in: Journal of Cardiothoracic Surgery | Issue 1/2017

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Abstract

Background

Solitary fibrous tumors of the pleura (SFTPs) are relatively rare tumors that originate from mesenchymal cells of submesothelial tissue of the pleura. Most patients with SFTPs are asymptomatic; however, pleuritic chest pain, cough, and dyspnea can develop. If hypoglycemia is associated with a solitary fibrous tumor, it is referred to as the Doege-Potter syndrome.

Case presentation

A 70-year-old man had visited our hospital with a chief complaint of dyspnea, and he was diagnosed as having a solitary fibrous tumor. A few years later, he developed hypoglycemia, and he underwent excision of the mass.

Conclusion

Occasionally, SFTPs induce several paraneoplastic events, such as hypertrophic osteoarthropathy. We described here a patient with an SFTP with Doege-Potter syndrome who was successfully treated with complete resection. Although lesions can be histologically benign, they can clinically present with malignant features.
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Metadata
Title
Doege-potter syndrome: a report of a histologically benign but clinically malignant case
Authors
Do Wan Kim
Kook Joo Na
Ju Sik Yun
Sang Yun Song
Publication date
01-12-2017
Publisher
BioMed Central
Published in
Journal of Cardiothoracic Surgery / Issue 1/2017
Electronic ISSN: 1749-8090
DOI
https://doi.org/10.1186/s13019-017-0630-4

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