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Open Access 01-12-2015 | Case report

PEComa of the uterus with coexistence of situs inversus totalis, a case report and literature review

Authors: Yang Han, Ting-ting Liu, Xue-shan Qiu, Qing-chang Li, Yi Zhao, Xiao-Yan Pang, En-hua Wang

Published in: Diagnostic Pathology | Issue 1/2015

Abstract

PEComas are a group of very rare mesenchymal neoplasms, which express myogenic and melanocytic markers, such as HMB-45 and actin. Situs inversus totalis represents a complete left to right side transposition of the asymmetrical thoracic and abdominal organs and incorporates dextrocardia. The presence of uterus PEComa in the setting of situs inversus totalis is extremely rare. Here, we report a case of PEComa of uterus with coexistence of situs inversus totalis and review the literatures. To the best of our knowledge this is the fist report of a uterus PEComa patient with situs inversus totalis.

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Title: PEComa of the uterus with coexistence of situs inversus totalis, a case report and literature review
Authors: Yang Han
Ting-ting Liu
Xue-shan Qiu
Qing-chang Li
Yi Zhao
Xiao-Yan Pang
En-hua Wang
Publication date: 01-12-2015
Publisher: BioMed Central
Published in: Diagnostic Pathology / Issue 1/2015
Electronic ISSN: 1746-1596
DOI: https://doi.org/10.1186/s13000-015-0351-8

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

PEComa of the uterus with coexistence of situs inversus totalis, a case report and literature review

Abstract

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

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