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Open Access 01-12-2016 | Review

PFAPA syndrome: a review on treatment and outcome

Authors: Federica Vanoni, Katerina Theodoropoulou, Michaël Hofer

Published in: Pediatric Rheumatology | Issue 1/2016

Abstract

The syndrome of periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA syndrome) is the most common cause of periodic fever in childhood. The current pharmacological treatment includes corticosteroids, which usually are efficacious in the management of fever episodes, colchicine, for the prophylaxis of febrile episodes, and other medication for which efficacy has not been proven so far. Tonsillectomy is an option for selected patients. Usually PFAPA syndrome resolves during adolescence, but there is increasing evidence that this condition may persist into adulthood.

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Title: PFAPA syndrome: a review on treatment and outcome
Authors: Federica Vanoni
Katerina Theodoropoulou
Michaël Hofer
Publication date: 01-12-2016
Publisher: BioMed Central
Published in: Pediatric Rheumatology / Issue 1/2016
Electronic ISSN: 1546-0096
DOI: https://doi.org/10.1186/s12969-016-0101-9

At a glance: The STEP trials

Springer Medicine

PFAPA syndrome: a review on treatment and outcome

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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