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Open Access 01-12-2018 | Case report

Robotic enucleation for pediatric insulinoma with MEN1 syndrome: a case report and literature review

Authors: Mei Liang, Jialin Jiang, Hongmei Dai, Xiafei Hong, Xianlin Han, Lin Cong, Anli Tong, Fang Li, Yaping Luo, Weinan Liu, Liangrui Zhou, Wenyu Di, Wenming Wu, Yupei Zhao

Published in: BMC Surgery | Issue 1/2018

Abstract

Background

A patient with a rare pediatric insulinoma and MEN1 syndrome was treated by robotic enucleation surgery.

Case presentation

We present a case of a 9-year-old girl presenting with repeated loss of consciousness, concomitant with a pale face, palpitations, and convulsions, which had persisted for 2 years and had been aggravated during the previous 2 months. She was previously misdiagnosed with epilepsy in another hospital. We further examined her while she was hospitalized. By combining her medical history and imaging examination and lab test results, a diagnosis of insulinoma was confirmed. Sanger-directed sequencing on a peripheral blood sample revealed an MEN1 gene mutation, indicating pediatric insulinoma with MEN1 syndrome. The patient underwent minimally invasive insulinoma enucleation surgery under the Da Vinci robot-assisted system with intraoperative ultrasound (IOUS) connected. The surgery was successfully completed within 65 min, and the girl recovered well postoperatively and no longer experienced symptoms of hypoglycemia.

Conclusion

This is the first report of a case of pediatric insulinoma treated using robotic enucleation. This experience demonstrates the feasibility and safety of combining robotic surgery with the enucleation procedure as an excellent strategy for pediatric insulinoma.

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Title: Robotic enucleation for pediatric insulinoma with MEN1 syndrome: a case report and literature review
Authors: Mei Liang
Jialin Jiang
Hongmei Dai
Xiafei Hong
Xianlin Han
Lin Cong
Anli Tong
Fang Li
Yaping Luo
Weinan Liu
Liangrui Zhou
Wenyu Di
Wenming Wu
Yupei Zhao
Publication date: 01-12-2018
Publisher: BioMed Central
Published in: BMC Surgery / Issue 1/2018
Electronic ISSN: 1471-2482
DOI: https://doi.org/10.1186/s12893-018-0376-5

ACC 2024 Congress

Springer Medicine

Robotic enucleation for pediatric insulinoma with MEN1 syndrome: a case report and literature review

Abstract

Background

Case presentation

Conclusion

ACC 2024 Congress

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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