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Published in: BMC Musculoskeletal Disorders 1/2020

Open Access 01-12-2020 | Research article

Deformity progression in congenital posteromedial bowing of the tibia: a report of 44 cases

Authors: Giovanni Luigi Di Gennaro, Giovanni Gallone, Edgar Alejandro Martinez Vazquez, Leonardo Marchesini Reggiani, Costantina Racano, Eleonora Olivotto, Stefano Stilli, Giovanni Trisolino

Published in: BMC Musculoskeletal Disorders | Issue 1/2020

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Abstract

Background

congenital posteromedial bowing of tibia (CPMBT) is a very rare birth defect, characterized by shortened bowed leg and ankle deformity. We described a single institution experience in the management of CPMBT.

Methods

we identified 44 CPMBT in 44 children. The age at presentation was 5.5 ± 5.6 years and the mean age at the final review was 10.1 ± 4.8 years. Radiographic evaluation included the antero-posterior and lateral inter-physeal angle (AP-IPA and L-IPA), the limb length discrepancy (LLD), the morphology of the distal tibia and the lateral distal tibial angle (LDTA). During the study period, 26 children underwent surgical treatment.

Results

the estimated curves showed a progressive spontaneous correction of both AP-IPA and L-IPA during growth, but a progressive increase of the LLD. The L-IPA showed a more predictable behaviour while the AP-IPA showed a scattered correction, with a wider variation of the estimated final angle. The final LDTA was 85.3° ± 4.2° and was correlated with the L-IPA (r = 0.5; p = 0.02).
Among the 26 children who underwent surgical treatment, 23 cases had limb lengthening, 1 case had contralateral epiphysiodesis, 1 child underwent tibial osteotomy, 1 patient was treated by hemiepiphysiodesis of the distal tibia to correct ankle valgus deformity.

Conclusions

our study described the largest case series of CPMBT. A combination of surgical treatments, in a staged surgical process, should be tailored to the developmental characteristics of this abnormality. An experience-based algorithm of treatment is also proposed. Further studies are needed to understand which is the best strategy to correct this deformity during childhood.

Level of evidence

level IV prognostic study.
Appendix
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Metadata
Title
Deformity progression in congenital posteromedial bowing of the tibia: a report of 44 cases
Authors
Giovanni Luigi Di Gennaro
Giovanni Gallone
Edgar Alejandro Martinez Vazquez
Leonardo Marchesini Reggiani
Costantina Racano
Eleonora Olivotto
Stefano Stilli
Giovanni Trisolino
Publication date
01-12-2020
Publisher
BioMed Central
Published in
BMC Musculoskeletal Disorders / Issue 1/2020
Electronic ISSN: 1471-2474
DOI
https://doi.org/10.1186/s12891-020-03408-w

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