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BMC Ophthalmology

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Open Access 01-12-2017 | Case report

Cystoid macular oedema associated with Rosai–Dorfman disease: a case report

Authors: Rubens Camargo Siqueira, Antonio Augusto Velasco e Cruz

Published in: BMC Ophthalmology | Issue 1/2017

Abstract

Background

The aim of this study is to report a case of cystoid macular oedema (CME) associated with Rosai–Dorfman Disease (RDD).

Case presentation

A 52-year-old male initially presented with a two-month history of a congested left eye. At presentation, visual acuity was 20/20 in the right eye and 20/80 in the left eye. Biomicroscopy showed conjunctival hyperaemia in the left eye with a slight elevation, suggesting a subconjunctival mass. Retinal fluorescein angiography and optical coherence tomography (OCT) revealed the presence of CME in the left eye. A clinical examination revealed nodular lesions in the ears and a lump in the subcutaneous tissue of the left arm. A biopsy of the subcutaneous lesion showed histological and immunohistochemical characteristics of RDD. The patient was treated with intravitreal triamcinolone (0.1 mL/4 mg). One month after treatment, there was complete regression of the oedema with a significant improvement in visual acuity to 20/20.

Conclusions

This is the first reported case of RDD associated with cystoid macular oedema. Macular oedema responded to intravitreal treatment with triamcinolone.

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Title: Cystoid macular oedema associated with Rosai–Dorfman disease: a case report
Authors: Rubens Camargo Siqueira
Antonio Augusto Velasco e Cruz
Publication date: 01-12-2017
Publisher: BioMed Central
Published in: BMC Ophthalmology / Issue 1/2017
Electronic ISSN: 1471-2415
DOI: https://doi.org/10.1186/s12886-017-0538-8

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Cystoid macular oedema associated with Rosai–Dorfman disease: a case report

Abstract

Background

Case presentation

Conclusions

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Background

Case presentation

Conclusions

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