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Published in: Journal of Medical Case Reports 1/2012

Open Access 01-12-2012 | Case report

Extraskeletal multiple myeloma presenting with an atrial mass: a case report and a review of the literature

Authors: Federica Vigo, Patrizia Ciammella, Riccardo Valli, Elisabetta Cagni, Cinzia Iotti

Published in: Journal of Medical Case Reports | Issue 1/2012

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Abstract

Introduction

Extraskeletal presentation at diagnosis or during the course of multiple myeloma is a rare event. The prognosis is usually very poor. At the moment there is no agreed gold standard for the treatment of this presentation.

Case presentation

A 79-year-old Caucasian woman was treated at our hospital for right atrial myeloma localization. Our patient showed the following signs and symptoms of congestive heart failure: dyspnea, hypotension, cyanosis and facial edema. Surgery was not considered feasible due to the extent of the disease. Our patient underwent external-beam radiation therapy using an intensity modulated technique, thus obtaining a persistent complete remission. Our patient has been in continuous complete local remission for 25 months since the end of radiotherapy.

Conclusion

The role of radiotherapy is not defined in multiple myeloma with extraskeletal presentation. Our regimen seems to be effective in controlling the disease in this patient.
This case report adds to the existing literature as it describes an unusual presentation of the disease and a new therapeutic approach to this rare presentation of multiple myeloma.
Appendix
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Metadata
Title
Extraskeletal multiple myeloma presenting with an atrial mass: a case report and a review of the literature
Authors
Federica Vigo
Patrizia Ciammella
Riccardo Valli
Elisabetta Cagni
Cinzia Iotti
Publication date
01-12-2012
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2012
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-6-236

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