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Published in: Journal of Medical Case Reports 1/2012

Open Access 01-12-2012 | Case report

Management strategy after diagnosis of Abernethy malformation: a case report

Authors: Caroline D. M. Witjes, Jan N. M. Ijzermans, Anton Vonk Noordegraaf, T. C. Khe Tran

Published in: Journal of Medical Case Reports | Issue 1/2012

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Abstract

Introduction

The Abernethy malformation is a rare anomaly with a widely variable clinical presentation. Many diagnostic dilemmas have been reported. Nowadays, with the evolution of medical imaging, diagnosis can be made more easily, but management of patients with an Abernethy malformation is still open for discussion.

Case presentation

In this case study, we describe a 34-year-old Caucasian man who presented with a large hepatocellular carcinoma in the presence of an Abernethy malformation, which was complicated by the development of pulmonary arterial hypertension.

Conclusion

This case underlines the importance of regular examination of patients with an Abernethy malformation, even in older patients, to prevent complications and to detect liver lesions at an early stage.
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Metadata
Title
Management strategy after diagnosis of Abernethy malformation: a case report
Authors
Caroline D. M. Witjes
Jan N. M. Ijzermans
Anton Vonk Noordegraaf
T. C. Khe Tran
Publication date
01-12-2012
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2012
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-6-167

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