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Published in: Journal of Medical Case Reports 1/2011

Open Access 01-12-2011 | Case report

An intracranial extramedullary hematopoiesis in a 34-year-old man with beta thalassemia: a case report

Authors: Homayoun Tabesh, Ahmad Shekarchizadeh, Parvin Mahzouni, Mojgan Mokhtari, Saeid Abrishamkar, Salman Abbasi Fard

Published in: Journal of Medical Case Reports | Issue 1/2011

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Abstract

Introduction

Extramedullary hematopoiesis occurs in approximately 15% of cases of thalassemia. Intracranial deposits of extramedullary hematopoiesis are an extremely rare compensatory process in intermediate and severe thalassemia.

Case presentation

We present an unusual case of an intracranial extramedullary hematopoiesis with a choroid plexus origin in a 34-year-old Caucasian man with beta thalassemia intermedia, who presented with the complaints of chronic headache and rapid progressive visual loss.

Conclusion

An intracranial extramedullary hematopoiesis, although extremely rare, should be considered as a potential ancillary diagnosis in any thalassemic patient and therefore appropriate studies should be performed to investigate the probable intracranial ectopic marrow before any surgical intervention.
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Metadata
Title
An intracranial extramedullary hematopoiesis in a 34-year-old man with beta thalassemia: a case report
Authors
Homayoun Tabesh
Ahmad Shekarchizadeh
Parvin Mahzouni
Mojgan Mokhtari
Saeid Abrishamkar
Salman Abbasi Fard
Publication date
01-12-2011
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2011
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-5-580

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