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Orphanet Journal of Rare Diseases
Published in: Orphanet Journal of Rare Diseases 1/2014

Open Access 01-12-2014 | Letter to the Editor

Development of interactive algorithm for clinical management of acute events related to sickle cell disease in emergency department

Authors: Gian Luca Forni, Gabriele Finco, Giovanna Graziadei, Manuela Balocco, Paolo Rigano, Silverio Perrotta, Oliviero Olivieri, Maria Domenica Cappellini, Lucia De Franceschi

Published in: Orphanet Journal of Rare Diseases | Issue 1/2014

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Abstract

Sickle cell disease (SCD ORPHA232; OMIM 603903) is a rare hereditary red cell disorder, which global distribution is changed in the last decade due to immigration-fluxes from endemic areas to Western-countries. One of the main clinical manifestations of SCD are the acute painful vaso-occlusive crisis, which cause frequent accesses of SCD patients to the emergency departments (EDs). This has generated the requirement of feasible tools for emergency givers. In the context of the scientific-Italian-Society for the study of Thalassemias and Hemoglobinopathies (SITE), we developed an algorithm with interactive windows to guide physicians in managing SCD patients in EDs.
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Metadata
Title
Development of interactive algorithm for clinical management of acute events related to sickle cell disease in emergency department
Authors
Gian Luca Forni
Gabriele Finco
Giovanna Graziadei
Manuela Balocco
Paolo Rigano
Silverio Perrotta
Oliviero Olivieri
Maria Domenica Cappellini
Lucia De Franceschi
Publication date
01-12-2014
Publisher
BioMed Central
Published in
Orphanet Journal of Rare Diseases / Issue 1/2014
Electronic ISSN: 1750-1172
DOI
https://doi.org/10.1186/1750-1172-9-91

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