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Pediatric Rheumatology

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Open Access 01-12-2009 | Case Report

Nummular keratopathy in a patient with Hyper-IgD Syndrome

Authors: Courtney L Kraus, Susan M Culican

Published in: Pediatric Rheumatology | Issue 1/2009

Abstract

Purpose

To report a case of recurrent nummular keratitis in a pediatric patient with Hyperimmunoglobulinemia D syndrome.

Methods

A retrospective chart review.

Results

A 14-year-old boy with Hyperimmunoglobulinemia D syndrome (HIDS) presented with photophobia and ocular irritation concomitant with disease exacerbation. He was found on exam to have significant nummular keratitis, which responded to a short course of topical steroids. Despite acute response to local immunosuppression, the patient had several recurrent attacks and eventually developed a large corneal scar and decreased vision. After initiation of infliximab therapy his ocular sequelae improved dramatically and his vision returned to 20/20.

Conclusion

One possible form of end-organ damage associated with HIDS is vision threatening nummular keratopathy.

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Title: Nummular keratopathy in a patient with Hyper-IgD Syndrome
Authors: Courtney L Kraus
Susan M Culican
Publication date: 01-12-2009
Publisher: BioMed Central
Published in: Pediatric Rheumatology / Issue 1/2009
Electronic ISSN: 1546-0096
DOI: https://doi.org/10.1186/1546-0096-7-14

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Nummular keratopathy in a patient with Hyper-IgD Syndrome

Abstract

Purpose

Methods

Results

Conclusion

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Purpose

Methods

Results

Conclusion

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