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Pediatric Rheumatology
Published in: Pediatric Rheumatology 1/2007

Open Access 01-12-2007 | Case Report

Rhupus arthropathy as the presenting manifestation in Juvenile SLE: a case report

Authors: Erbil Unsal, Ayse Ozgun Arlı, Hakkı Akman

Published in: Pediatric Rheumatology | Issue 1/2007

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Abstract

An 8.5-year-old girl was referred with swelling of both knees lasting for two years. ANA was found as negative. She was diagnosed as oligoarticular JIA. After two years of follow-up, thrombocytopenia was detected during routine screening. Her ANA and anti ds-DNA antibodies also became positive, with low levels of C3 and C4. She was diagnosed as Juvenile SLE, meeting the criteria cytopenia, positive immunoserology (anti dsDNA), positive ANA test, and four years of ongoing chronic arthritis, so called as "rhupus arthropathy". We should be aware of the several initial incomplete presentations of lupus in children. We should be careful in monitoring the serious manifestations of the disease in juvenile lupus patients with rhupus arthropathy, and consider the poor response to standard disease modifying agents.
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Metadata
Title
Rhupus arthropathy as the presenting manifestation in Juvenile SLE: a case report
Authors
Erbil Unsal
Ayse Ozgun Arlı
Hakkı Akman
Publication date
01-12-2007
Publisher
BioMed Central
Published in
Pediatric Rheumatology / Issue 1/2007
Electronic ISSN: 1546-0096
DOI
https://doi.org/10.1186/1546-0096-5-7

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