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Published in: BMC Pediatrics 1/2004

Open Access 01-12-2004 | Case report

Abnormal systemic venous connection possibly associated with a persistent right umbilical vein; a case report

Authors: Britt Nakstad, Bjarne Smevik

Published in: BMC Pediatrics | Issue 1/2004

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Abstract

Background

Abnormal venous connections involving a persistent right umbilical vein are rare. In a minority of cases the liver is entirely bypassed and the condition is associated with multiple congenital malformations.

Case presentation

The described case illustrates a systemic venous drainage that was severely abnormal in a newborn girl with a truncus arteriosus type II congenital heart defect. Injection of contrast medium through the umbilical vein catheter revealed a very peculiar venous connection that passed anterio-laterally through the right hemithorax before crossing in an oblique fashion towards the superior vena cava.

Conclusions

This venous drainage may be the result of a persistent right umbilical vein connecting with the superior vena cava.
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Metadata
Title
Abnormal systemic venous connection possibly associated with a persistent right umbilical vein; a case report
Authors
Britt Nakstad
Bjarne Smevik
Publication date
01-12-2004
Publisher
BioMed Central
Published in
BMC Pediatrics / Issue 1/2004
Electronic ISSN: 1471-2431
DOI
https://doi.org/10.1186/1471-2431-4-7

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