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Published in: BMC Neurology 1/2010

Open Access 01-12-2010 | Case report

Systemic panca-associated vasculitis with central nervous involvement causing recurrent myelitis: case report

Authors: Alexander J Hamilton, Duncan J Whitehead, Matthew D Bull, Richard J D'Souza

Published in: BMC Neurology | Issue 1/2010

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Abstract

Background

We report on the case of an established perinuclear antineutrophil cytoplasmic antibody (pANCA) associated renal vasculitis being treated with prednisolone and rituximab, where the patient presented with leg weakness, urinary and faecal incontinence and buttock pain consistent with transverse myelitis.

Case presentation

The patient underwent MRI scanning showing patchy cord enhancement from T10 to the conus, which was suggestive of a cord malignancy. Prior to a cord biopsy, he was treated with steroids and a repeat MRI showed resolution of the original lesion with a new similar lesion from C7 to T3.

Conclusions

He made a marked recovery after further treatment with high dose steroids and plasma exchange.
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Metadata
Title
Systemic panca-associated vasculitis with central nervous involvement causing recurrent myelitis: case report
Authors
Alexander J Hamilton
Duncan J Whitehead
Matthew D Bull
Richard J D'Souza
Publication date
01-12-2010
Publisher
BioMed Central
Published in
BMC Neurology / Issue 1/2010
Electronic ISSN: 1471-2377
DOI
https://doi.org/10.1186/1471-2377-10-118

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