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Open Access 01-12-2018 | Case report

Late presentation, MR imaging features and surgical treatment of Herlyn-Werner-Wunderlich syndrome (classification 2.2); a case report

Published in: BMC Women's Health | Issue 1/2018

Abstract

Background

Herlyn-Werner-Wunderlich syndrome is a very rare congenital genitourinary anomaly characterized by uterus didelphys, blind hemivagina and ipsilateral renal agenesis.

Case presentation

Authors present a case of Herlyn-Werner-Wunderlich syndrome in a 19-year-old unmarried woman who presented with pelvic pain and pelvic mass. MR imaging revealed the typical features of didelphys uterus, obstructed right hemivagina and ipsilateral renal agenesis. The patient subsequently underwent surgery.

Conclusions

Herlyn-Werner-Wunderlich syndrome would be suspected in patients with unilateral absent kidney and pelvic mass. Ultrasonography and MR imaging can well depict the disease entity and surgery is the treatment of choice for obstructed hemivagina.

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Ahmad Z, Goyal A, Das CJ, Deka D, Sharma R. Herlyn–Werner–Wunderlich syndrome presenting with infertility: role of MRI in diagnosis. Indian J Radiol Imaging. 2013;23(3):243.CrossRef

Gholoum S, Puligandla PS, Hui T, Su W, Quiros E, Laberge JM. Management and outcome of patients with combined vaginal septum, bifid uterus, and ipsilateral renal agenesis (Herlyn-Werner-Wunderlich syndrome). J Pediatr Surg. 2006;41(5):987–92.CrossRef

Title: Late presentation, MR imaging features and surgical treatment of Herlyn-Werner-Wunderlich syndrome (classification 2.2); a case report
Publication date: 01-12-2018
Published in: BMC Women's Health / Issue 1/2018
Electronic ISSN: 1472-6874
DOI: https://doi.org/10.1186/s12905-018-0655-4

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Late presentation, MR imaging features and surgical treatment of Herlyn-Werner-Wunderlich syndrome (classification 2.2); a case report

Abstract

Background

Case presentation

Conclusions

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusions

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