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Published in: Italian Journal of Pediatrics 1/2010

Open Access 01-12-2010 | Case report

Peculiar type 1 congenital pyloric atresia: a case report

Authors: Enrico Zecca, Mirta Corsello, Claudio Pintus, Lorenzo Nanni, Susanna Zecca

Published in: Italian Journal of Pediatrics | Issue 1/2010

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Abstract

Pyloric atresia (PA) is a very rare condition. Its incidence is approximately 1 in 100,000 newborns and constitutes about 1% of all intestinal atresias. We describe the neonatal course of a peculiar case of type 1 pyloric atresia, in which the pyloric membrane was connected to a second duodenal membrane through a virtual duodenal lumen in a premature newborn. The atypical variant required an unusual side to side gastroduodenostomy. We emphasize the importance of a prompt diagnosis to avoid potentially fatal complications and to warrant a good outcome even in the presence of a strange form of PA in the neonatal period.
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Metadata
Title
Peculiar type 1 congenital pyloric atresia: a case report
Authors
Enrico Zecca
Mirta Corsello
Claudio Pintus
Lorenzo Nanni
Susanna Zecca
Publication date
01-12-2010
Publisher
BioMed Central
Published in
Italian Journal of Pediatrics / Issue 1/2010
Electronic ISSN: 1824-7288
DOI
https://doi.org/10.1186/1824-7288-36-3

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