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Published in: Thyroid Research 1/2013

Open Access 01-12-2013 | Review

Management of hyperparathyroidism (PHP) in MEN2 syndromes in Europe

Author: Maria Alevizaki

Published in: Thyroid Research | Special Issue 1/2013

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Abstract

Hyperparathyroidism occurs in 20-30% of MEN2A syndrome patients. It is usually associated with mild disease and is frequently asymptomatic, especially in younger age. There is genotype/phenotype association and PHP is usually associated with codon 634 mutations; however association with more “rare” mutations has also been reported. The pathology of the parathyroid glands includes hyperplasia, adenoma or a combination of the two. The optimal surgical management of this entity has not been defined yet.
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Metadata
Title
Management of hyperparathyroidism (PHP) in MEN2 syndromes in Europe
Author
Maria Alevizaki
Publication date
01-12-2013
Publisher
BioMed Central
Published in
Thyroid Research / Issue Special Issue 1/2013
Electronic ISSN: 1756-6614
DOI
https://doi.org/10.1186/1756-6614-6-S1-S10

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