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Published in: Orphanet Journal of Rare Diseases 1/2007

Open Access 01-12-2007 | Research

Health status of adults with Short Stature: A comparison with the normal population and one well-known chronic disease (Rheumatoid Arthritis)

Authors: Heidi Johansen, Inger-Lise Andresen, Eva E Naess, Kare Birger Hagen

Published in: Orphanet Journal of Rare Diseases | Issue 1/2007

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Abstract

Background

To examine the subjective health status of adults with short stature (ShSt) and compare with the general population (GP) and one well-known chronic disease, rheumatoid artritis (RA). In addition, to explore the association between age, gender, height, educational level and different aspects of health status of adults with short stature.

Methods

A questionnaire was mailed to 72 subjects with short stature registered in the database of a Norwegian resource centre for rare disorders, response rate 61% (n = 44, age 16–61). Health status was assessed with SF-36 version 2. Comparison was done with age and gender matched samples from the general population in Norway (n = 264) and from subjects with RA (n = 88).

Results

The ShSt sample reported statistically significant impaired health status in all SF-36 subscales compared with the GP sample, most in the physical functioning, Mean Difference (MD) 34 (95% Confidence Interval (CI) 25–44). The ShSt reported poorer health status in mental health, MD 11 (95% CI 4–18) and social functioning, MD 11 (95% CI 2–20) but better in role physical MD 13 (95% CI 1–25) than the RA sample. On the other subscales there were minor difference between the ShSt and the RA sample. Within the short stature group there was a significant association between age and all SF-36 physical subcales, height was significantly associated with physical functioning while level of education was significantly associated with mental health.

Conclusion

People with short stature reported impaired health status in all SF-36 subscales indicating that they have health problems that influence their daily living. Health status seems to decline with increasing age, and earlier than in the general population.
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Metadata
Title
Health status of adults with Short Stature: A comparison with the normal population and one well-known chronic disease (Rheumatoid Arthritis)
Authors
Heidi Johansen
Inger-Lise Andresen
Eva E Naess
Kare Birger Hagen
Publication date
01-12-2007
Publisher
BioMed Central
Published in
Orphanet Journal of Rare Diseases / Issue 1/2007
Electronic ISSN: 1750-1172
DOI
https://doi.org/10.1186/1750-1172-2-10

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