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Journal of Cardiothoracic Surgery
Published in: Journal of Cardiothoracic Surgery 1/2011

Open Access 01-12-2011 | Case report

Successful surgical excision of primary right atrial angiosarcoma

Authors: Wobbe Bouma, Chris PH Lexis, Tineke P Willems, Albert JH Suurmeijer, Iwan CC van der Horst, Tjark Ebels, Massimo A Mariani

Published in: Journal of Cardiothoracic Surgery | Issue 1/2011

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Abstract

Primary cardiac angiosarcoma is a rare and aggressive tumor with a high incidence of metastatic spread (up to 89%) at the time of diagnosis, which restricts the indication for surgical resection to a small number of patients. We report the case of a 50-year old Caucasian woman with non-metastatic primary right atrial angiosarcoma, who underwent successful surgical excision of the tumor (with curative intent) and reconstruction of the right atrium with a porcine pericardial patch. However, after a symptom-free survival of five months the patient presented with bone and liver metastases without evidence of local tumor recurrence.
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Metadata
Title
Successful surgical excision of primary right atrial angiosarcoma
Authors
Wobbe Bouma
Chris PH Lexis
Tineke P Willems
Albert JH Suurmeijer
Iwan CC van der Horst
Tjark Ebels
Massimo A Mariani
Publication date
01-12-2011
Publisher
BioMed Central
Published in
Journal of Cardiothoracic Surgery / Issue 1/2011
Electronic ISSN: 1749-8090
DOI
https://doi.org/10.1186/1749-8090-6-47

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