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Open Access 01-12-2010 | Case report

Steroid responsive encephalopathy in cerebral amyloid angiopathy: a case report and review of evidence for immunosuppressive treatment

Authors: Raoul P Kloppenborg, Edo Richard, Marieke ES Sprengers, Dirk Troost, Piet Eikelenboom, Paul J Nederkoorn

Published in: Journal of Neuroinflammation | Issue 1/2010

Abstract

Cerebral amyloid angiopathy (CAA) is a common but often asymptomatic disease, characterized by deposition of amyloid in cerebral blood vessels. We describe the successful treatment of CAA encephalopathy with dexamethasone in a patient with CAA-related inflammation causing subacute progressive encephalopathy and seizures, which is an increasingly recognized subtype of CAA. The two pathological subtypes of CAA-related inflammation are described and a review of the literature is performed concerning immunosuppressive treatment of CAA-related inflammation with special attention to its pathological subtypes. Immunosuppressive therapy appears to be an appropriate treatment for CAA encephalopathy.

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Title: Steroid responsive encephalopathy in cerebral amyloid angiopathy: a case report and review of evidence for immunosuppressive treatment
Authors: Raoul P Kloppenborg
Edo Richard
Marieke ES Sprengers
Dirk Troost
Piet Eikelenboom
Paul J Nederkoorn
Publication date: 01-12-2010
Publisher: BioMed Central
Published in: Journal of Neuroinflammation / Issue 1/2010
Electronic ISSN: 1742-2094
DOI: https://doi.org/10.1186/1742-2094-7-18

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Steroid responsive encephalopathy in cerebral amyloid angiopathy: a case report and review of evidence for immunosuppressive treatment

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

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