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Open Access 01-12-2010 | Review

HAE international home therapy consensus document

Authors: Hilary J Longhurst, Henriette Farkas, Timothy Craig, Emel Aygören-Pürsün, Claire Bethune, Janne Bjorkander, Konrad Bork, Laurence Bouillet, Henrik Boysen, Anette Bygum, Teresa Caballero, Marco Cicardi, John Dempster, Mark Gompels, Jimmy Gooi, Sofia Grigoriadou, Ursula Huffer, Wolfhart Kreuz, Marcel M Levi, Janet Long, Inmaculada Martinez-Saguer, Michel Raguet, Avner Reshef, Tom Bowen, Bruce Zuraw

Published in: Allergy, Asthma & Clinical Immunology | Issue 1/2010

Abstract

Hereditary angioedema (C1 inhibitor deficiency, HAE) is associated with intermittent swellings which are disabling and may be fatal. Effective treatments are available and these are most useful when given early in the course of the swelling. The requirement to attend a medical facility for parenteral treatment results in delays. Home therapy offers the possibility of earlier treatment and better symptom control, enabling patients to live more healthy, productive lives. This paper examines the evidence for patient-controlled home treatment of acute attacks ('self or assisted administration') and suggests a framework for patients and physicians interested in participating in home or self-administration programmes. It represents the opinion of the authors who have a wide range of expert experience in the management of HAE.

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Title: HAE international home therapy consensus document
Authors: Hilary J Longhurst
Henriette Farkas
Timothy Craig
Emel Aygören-Pürsün
Claire Bethune
Janne Bjorkander
Konrad Bork
Laurence Bouillet
Henrik Boysen
Anette Bygum
Teresa Caballero
Marco Cicardi
John Dempster
Mark Gompels
Jimmy Gooi
Sofia Grigoriadou
Ursula Huffer
Wolfhart Kreuz
Marcel M Levi
Janet Long
Inmaculada Martinez-Saguer
Michel Raguet
Avner Reshef
Tom Bowen
Bruce Zuraw
Publication date: 01-12-2010
Publisher: BioMed Central
Published in: Allergy, Asthma & Clinical Immunology / Issue 1/2010
Electronic ISSN: 1710-1492
DOI: https://doi.org/10.1186/1710-1492-6-22

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HAE international home therapy consensus document

Abstract

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