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Open Access 01-12-2008 | Case Report

Aggressive immunosuppressive treatment of Susac's syndrome in an adolescent: using treatment of dermatomyositis as a model

Authors: Robert M Rennebohm, Martin Lubow, Jerome Rusin, Lisa Martin, Deborah M Grzybowski, John O Susac

Published in: Pediatric Rheumatology | Issue 1/2008

Abstract

We describe aggressive immunosuppressive treatment of an adolescent with Susac's syndrome (SS), a disease of the microvasculature in the brain, retina, and inner ear. Because the immunopathogenesis of SS appears to have much in common with that of juvenile dermatomyositis (JDM), the patient was treated with an approach that has been effective for severe JDM. The patient's outcome provides evidence for the importance of prompt, aggressive, and sustained immunosuppressive treatment of encephalopathic SS.

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Title: Aggressive immunosuppressive treatment of Susac's syndrome in an adolescent: using treatment of dermatomyositis as a model
Authors: Robert M Rennebohm
Martin Lubow
Jerome Rusin
Lisa Martin
Deborah M Grzybowski
John O Susac
Publication date: 01-12-2008
Publisher: BioMed Central
Published in: Pediatric Rheumatology / Issue 1/2008
Electronic ISSN: 1546-0096
DOI: https://doi.org/10.1186/1546-0096-6-3

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Aggressive immunosuppressive treatment of Susac's syndrome in an adolescent: using treatment of dermatomyositis as a model

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

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