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BMC Dermatology

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Open Access 01-12-2001 | Case report

Bilateral linear scleroderma "en coup de sabre" associated with facial atrophy and neurological complications

Authors: Thilo Gambichler, Alexander Kreuter, Klaus Hoffmann, Falk G Bechara, Peter Altmeyer, Thomas Jansen

Published in: BMC Dermatology | Issue 1/2001

Abstract

Background

Linear scleroderma "en coup de sabre" (LSCS) usually affects one side of the face and head in the frontoparietal area with band-like indurated skin lesions. The disease may be associated with facial hemiatrophy. Various ophthalmological and neurological abnormalities have been observed in patients with LSCS. We describe an unusual case of LSC.

Case presentation

A 23 year old woman presented bilateral LSCS and facial atrophy. The patient had epileptic seizures as well as oculomotor and facial nerve palsy on the left side which also had pronounced skin involvement. Clinical features of different stages of the disease are presented.

Conclusions

The findings of the presented patient with bilateral LSCS and facial atrophy provide further evidence for a neurological etiology of the disease and may also indicate that classic progressive facial hemiatrophy (Parry-Romberg syndrome) and LSCS actually represent different spectra of the same disease.

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The pre-publication history for this paper can be accessed here:http://www.biomedcentral.com/1471-5945/1/9/prepub

Title: Bilateral linear scleroderma "en coup de sabre" associated with facial atrophy and neurological complications
Authors: Thilo Gambichler
Alexander Kreuter
Klaus Hoffmann
Falk G Bechara
Peter Altmeyer
Thomas Jansen
Publication date: 01-12-2001
Publisher: BioMed Central
Published in: BMC Dermatology / Issue 1/2001
Electronic ISSN: 1471-5945
DOI: https://doi.org/10.1186/1471-5945-1-9

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Bilateral linear scleroderma "en coup de sabre" associated with facial atrophy and neurological complications

Abstract

Background

Case presentation

Conclusions

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusions

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