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BMC Surgery

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Open Access 01-12-2006 | Case report

Splenectomy and proximal lieno-renal shunt in a factor five deficient patient with extra-hepatic portal vein obstruction

Authors: Srinivas Prabhu Chava, Sujoy Pal, Supriyo Ghatak, Rajat Kumar, Peush Sahni, Tushar Kanti Chattopadhyay

Published in: BMC Surgery | Issue 1/2006

Abstract

Background

The clinico-surgical implication and successful management of a rare case of factor five (V) deficiency with portal hypertension and hypersplenism due to idiopathic extra-hepatic portal venous obstruction is presented.

Case presentation

A 16-year old boy had gastro-esophageal variceal bleeding, splenomegaly and hypersplenism. During preoperative workup prolonged prothrombin time and activated partial thromboplastin time were detected, which on further evaluation turned out to be due to factor V deficiency. Proximal lieno-renal shunt and splenectomy were successfully performed with transfusion of fresh frozen plasma during and after the surgical procedure. At surgery there was no excessive bleeding. The perioperative course was uneventful and the patient is doing well on follow up.

Conclusion

Surgical portal decompressive procedures can be safely undertaken in clotting factor deficient patients with portal hypertension if meticulous surgical hemostasis is achieved at operation and the deficient factor is adequately replaced in the perioperative period.

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The pre-publication history for this paper can be accessed here:http://www.biomedcentral.com/1471-2482/6/7/prepub

Title: Splenectomy and proximal lieno-renal shunt in a factor five deficient patient with extra-hepatic portal vein obstruction
Authors: Srinivas Prabhu Chava
Sujoy Pal
Supriyo Ghatak
Rajat Kumar
Peush Sahni
Tushar Kanti Chattopadhyay
Publication date: 01-12-2006
Publisher: BioMed Central
Published in: BMC Surgery / Issue 1/2006
Electronic ISSN: 1471-2482
DOI: https://doi.org/10.1186/1471-2482-6-7

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Splenectomy and proximal lieno-renal shunt in a factor five deficient patient with extra-hepatic portal vein obstruction

Abstract

Background

Case presentation

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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