An Uncommon Malignancy of the Breast; Dermatofibrosarcoma Protruberans- A Case Report

Excerpt

Dermatofibrosarcoma protruberans(DFSP) is rare, morphologically distinct dermal/ subcutaneous neoplasm [1]. It typically presents during early or mid adult life. It is most common in the trunk and extremities and it accounts for approximately 0.1 % of all cutaneous malignancies and 6 % of all soft tissue sarcomas [2‐4]. DFSP is highly aggressive, invades locally and rarely metastasizes [4]. Surgical scars, old burns, contractures and sites of vaccinations have all been reported as DFSP sites [5, 6]. DFSP occurring in the breast is very unusual. A review of literature reveals very few cases of DFSP breast. DFSP in the breast is usually characterized by smooth mobile raised reddish mass with brownish plaque like cutaneous thickening [6]. Treatment is primarily surgical, with chemotherapy and radiation therapy sometimes being used [6, 7]. …