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Published in: Journal of Maxillofacial and Oral Surgery 1/2024

26-03-2023 | Alopecia | CASE REPORT

Haberland Syndrome Associated with Juvenile Ossifying Fibroma and Odontoma: Rare Case Report

Authors: Ragavi Alagarsamy, Ongkila Bhutia, Ajoy Roychoudhury, Babu Lal, Rahul Yadav, Deepika Mishra

Published in: Journal of Maxillofacial and Oral Surgery | Issue 1/2024

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Excerpt

Encephalocraniocutaneous lipomatosis (ECCL) also known as Haberland syndrome is a rare neurocutaneous syndrome characterized by involvement of tissues of mesodermal and ectodermal origin such as skin, eyes, adipose tissue, and brain. This rare disorder was first reported in a 5 1/2-year-old epileptic, mentally retarded boy in 1970 by Catherine Haberland and Maurice Perou [1]. Since then around 70 cases have been reported worldwide as per our knowledge. …
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Metadata
Title
Haberland Syndrome Associated with Juvenile Ossifying Fibroma and Odontoma: Rare Case Report
Authors
Ragavi Alagarsamy
Ongkila Bhutia
Ajoy Roychoudhury
Babu Lal
Rahul Yadav
Deepika Mishra
Publication date
26-03-2023
Publisher
Springer India
Published in
Journal of Maxillofacial and Oral Surgery / Issue 1/2024
Print ISSN: 0972-8279
Electronic ISSN: 0974-942X
DOI
https://doi.org/10.1007/s12663-023-01893-9

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