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01-03-2012 | North American Society of Head and Neck Pathology Companion Meeting, March 18, 2012, Vancouver, British Columbia

Striking Pathology Gold: A Singular Experience with Daily Reverberations: Sinonasal Hemangiopericytoma (Glomangiopericytoma) and Oncogenic Osteomalacia

Authors: Margaret Brandwein-Gensler, Gene P. Siegal

Published in: Head and Neck Pathology | Issue 1/2012

Abstract

Sinonasal hemangiopericytoma-like tumors(SNHPC)(glomangiopericytomas)were originally conceived as histologically similar to, but biologically distinct from, their soft tissue counterparts. Re-evaluation of “hemangiopericytiomas” has determined that SNHPC (glomangiopericytomas) represent bona-fide pericyte-derived tumors, whereas most soft tissue neoplasms previously designated as hemangiopericytomas represent cellular variants of solitary fibrous tumors or other lesions with a hemangiopericytomalike growth pattern. We present an interesting case of a woman with SNHPC (glomangiopericytomas) causing oncogenic osteomalacia, and discuss the recent advances in our understanding of phosphaturic mesenchymal tumors. This particular case is an example of “Striking Pathology Gold”—a situation where the pathologist actively guides the diagnostic process, and witnesses its repercussions. “Striking Pathology Gold” may be a rare event in one’s career. However it serves to remind us of our place in the world as physicians. Working behind the scenes, we quietly change the course of countless individual destinies for the better.

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Title: Striking Pathology Gold: A Singular Experience with Daily Reverberations: Sinonasal Hemangiopericytoma (Glomangiopericytoma) and Oncogenic Osteomalacia
Authors: Margaret Brandwein-Gensler
Gene P. Siegal
Publication date: 01-03-2012
Publisher: Springer US
Published in: Head and Neck Pathology / Issue 1/2012
Electronic ISSN: 1936-0568
DOI: https://doi.org/10.1007/s12105-012-0337-8

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Striking Pathology Gold: A Singular Experience with Daily Reverberations: Sinonasal Hemangiopericytoma (Glomangiopericytoma) and Oncogenic Osteomalacia

Abstract

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

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