Top

Indian Journal of Thoracic and Cardiovascular Surgery

Published in:

01-04-2018 | Case report

Isolated right pulmonary agenesis with dextrocardia presenting in adulthood

Authors: Maruti Yamanappa Haranal, Satyaprakash Sanjeevaiah, Shashidhar Buggi

Published in: Indian Journal of Thoracic and Cardiovascular Surgery | Issue 2/2018

Abstract

Occurrence of right pulmonary agenesis in isolation is rare and carries a mortality rate of 50% during the first 5 years of life. The frequent association of congenital cardiac malformations with right pulmonary agenesis makes its prognosis bad. The diagnosis is challenging in those, who survive to adulthood because of nonspecific clinical presentations. Limited number of cases of isolated right pulmonary agenesis with dextrocardia in a structurally normal heart presenting in adulthood have been reported in the literature.

Mardini MK, Nyhan WL. Agenesis of the lung: report of four patients with unusual anomalies. Chest. 1985;87:522–7.CrossRefPubMed

Maltz DL, Nadas AS. Agenesis of the lung: presentation of eight new cases and review of the literature. Pediatrics. 1968;42:175–88.PubMed

Capuani A, Del Torso S, Lincoln JC. Right lung agenesis. A case report. G Ital Cardiol. 1982;12:381–3.PubMed

Kullmann F, Koch R, Feichtinger W, Giesen H, Schmid M, Grimm T. Holt-Oram syndrome in combination with reciprocal translocation, lung hypoplasia and cardiomyopathy. Klin Padiatr. 1993;205:185–9.CrossRefPubMed

Oymada A, Gasul BM, Holinger PM. Agenesis of the lung. Am J Dis Child. 1953;85:182–7.

Black PR, Welch KJ. Pulmonary agenesis (aplasia), oesophageal atresia, and tracheoesophageal fistula: a different treatment strategy. J Pediatr Surg. 1986;21:936–8.CrossRefPubMed

Koseoglu N, Ucan ES, Cavdar C.Right lung agenesis and left lung bronchiectasis. Respir Med Extra. 2005;1:110-12.

Yetim TD, Bayarogullari H, Yalçin HP, Arica V, Arica SG. Congenital agenesis of the left lung: a rare case. J Clin Imaging Sci. 2011;1:47.CrossRefPubMedPubMedCentral

Krivchenya DU, Dubrovin AG, Krivchenya TD, Khursin VN, Lysak CV. Aplasia of the right lung in a 4 year old child; surgical stabilization of the mediastinum by diaphragm translocation leading to complete recovery from respiratory distress syndrome. J Pediatr Surg. 2000;35:1499–502.CrossRefPubMed

10.

Bittigau K, Bohm J, Kursawe R, Nowotny T, Bittigau P, Konertz W. Pulmonary agenesis in a newborn: implantation of tissue expander to prevent a mediastinal shift. Thorac Cardiovasc Surg. 1995;43:287–9.CrossRefPubMed

Title: Isolated right pulmonary agenesis with dextrocardia presenting in adulthood
Authors: Maruti Yamanappa Haranal
Satyaprakash Sanjeevaiah
Shashidhar Buggi
Publication date: 01-04-2018
Publisher: Springer Singapore
Published in: Indian Journal of Thoracic and Cardiovascular Surgery / Issue 2/2018
Print ISSN: 0970-9134
Electronic ISSN: 0973-7723
DOI: https://doi.org/10.1007/s12055-017-0570-6

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Isolated right pulmonary agenesis with dextrocardia presenting in adulthood

Abstract

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Please log in to get access to this content

Other articles of this Issue 2/2018

Rare association of arteriovenous malformation of the big toe and ipsilateral aneurysms in the dorsalis pedis artery

Cardiac rehabilitation reduces salivary levels of interleukin-6 in post coronary artery bypass graft patients

Does body mass index influence pulmonary function test values and functional exercise capacity after chest physiotherapy following coronary artery bypass graft

Huge right subclavian artery aneurysm due to inadvertent trauma during percutaneous central venous catheter insertion

Incidental finding of coarctation of the aorta in a Marfan patient: a case report

Congenital eventration of diaphragm in an adult with dysmorphic face and digits