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Clinical Orthopaedics and Related Research®
Published in: Clinical Orthopaedics and Related Research® 9/2009

01-09-2009 | Case Report

Case Report: Kaposiform Hemangioendothelioma in Multiple Spinal Levels Without Skin Changes

Authors: Jennifer W. Lisle, MD, Heather A. Bradeen, MD, Alexandra N. Kalof, MD

Published in: Clinical Orthopaedics and Related Research® | Issue 9/2009

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Abstract

Kaposiform hemangioendothelioma is a rare vascular tumor of childhood that is locally aggressive but has little metastatic potential and by itself is not known to be lethal. It most commonly presents as a superficial or deep soft tissue mass with associated cutaneous lesions. Kasabach-Merritt phenomenon, a condition characterized by profound thrombocytopenia and life-threatening hemorrhage, often is associated with kaposiform hemangioendothelioma. Six cases of kaposiform hemangioendothelioma have been reported in bone, two of which were located in extracraniofacial bones. We report a diagnostically challenging case of a 6-year-old girl with kaposiform hemangioendothelioma of the thoracolumbar spine without Kasabach-Merritt phenomenon or cutaneous lesions.
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Metadata
Title
Case Report: Kaposiform Hemangioendothelioma in Multiple Spinal Levels Without Skin Changes
Authors
Jennifer W. Lisle, MD
Heather A. Bradeen, MD
Alexandra N. Kalof, MD
Publication date
01-09-2009
Publisher
Springer-Verlag
Published in
Clinical Orthopaedics and Related Research® / Issue 9/2009
Print ISSN: 0009-921X
Electronic ISSN: 1528-1132
DOI
https://doi.org/10.1007/s11999-009-0838-2

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