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General Thoracic and Cardiovascular Surgery
Published in: General Thoracic and Cardiovascular Surgery 12/2019

01-12-2019 | Rhabdomyosarcoma | Case Report

A rare resected case of pulmonary rhabdomyosarcoma

Authors: Yuki Nishioka, Shinya Tane, Wataru Nishio, Hiroki Tanaka, Hiroyuki Ogawa, Yoshitaka Kitamura, Toshiko Sakuma, Masahiro Yoshimura

Published in: General Thoracic and Cardiovascular Surgery | Issue 12/2019

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Abstract

Rhabdomyosarcoma is a well-known neoplasm in children that frequently occurs in the extremities, the head and neck region, and the genitourinary tract. To the best of our knowledge, pulmonary primary rhabdomyosarcoma in adults is exceedingly rare, and few resected cases have been reported. We report a case of pulmonary primary rhabdomyosarcoma that was surgically resected then treated with adjuvant chemotherapy (vincristine, actinomycin-D and cyclophosphamide). At 9 months after surgery, the patient is free from disease. Although the prognosis of rhabdomyosarcoma is unfavorable, surgical resection and adjuvant therapy could be a potential treatment strategy for pulmonary primary rhabdomyosarcoma.
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Metadata
Title
A rare resected case of pulmonary rhabdomyosarcoma
Authors
Yuki Nishioka
Shinya Tane
Wataru Nishio
Hiroki Tanaka
Hiroyuki Ogawa
Yoshitaka Kitamura
Toshiko Sakuma
Masahiro Yoshimura
Publication date
01-12-2019
Publisher
Springer Singapore
Published in
General Thoracic and Cardiovascular Surgery / Issue 12/2019
Print ISSN: 1863-6705
Electronic ISSN: 1863-6713
DOI
https://doi.org/10.1007/s11748-019-01086-7

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