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General Thoracic and Cardiovascular Surgery
Published in: General Thoracic and Cardiovascular Surgery 1/2017

01-01-2017 | Case Report

Orthotropic heart transplantation for adult congenital heart disease: a case with heterotaxy and dextrocardia

Authors: Hikaru Matsuda, Norihide Fukushima, Hajime Ichikawa, Yoshiki Sawa

Published in: General Thoracic and Cardiovascular Surgery | Issue 1/2017

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Abstract

A 41-year-old male with heterotaxy (left isomerism) and dextrocardia composed by single ventricle, absent inferior vena cava, bilateral superior vena cava (SVC), common atrioventricular valve has received orthotopic heart transplantation (HTx) after long waiting period as Status-1. Reconstructions of bilateral SVC and hepatic vein route were successful without use of prosthetic material, and the donor heart was placed in the left mediastinum. In spite of satisfactory early recovery, the patient expired 4 months after transplantation mainly from fungal infection which developed following humoral rejection. HTx for adult patients with complex congenital heart disease is demanding in technical as well as pre- and post-transplant management, and indication should be critically determined.
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Metadata
Title
Orthotropic heart transplantation for adult congenital heart disease: a case with heterotaxy and dextrocardia
Authors
Hikaru Matsuda
Norihide Fukushima
Hajime Ichikawa
Yoshiki Sawa
Publication date
01-01-2017
Publisher
Springer Japan
Published in
General Thoracic and Cardiovascular Surgery / Issue 1/2017
Print ISSN: 1863-6705
Electronic ISSN: 1863-6713
DOI
https://doi.org/10.1007/s11748-015-0573-4

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