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General Thoracic and Cardiovascular Surgery

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01-07-2016 | Case Report

Total pleural covering technique for intractable pneumothorax in patient with Ehlers–Danlos syndrome

Authors: Yoshihisa Kadota, Eriko Fukui, Naoto Kitahara, Eiji Okura, Mitsunori Ohta

Published in: General Thoracic and Cardiovascular Surgery | Issue 7/2016

Abstract

We report a patient with vascular-type Ehlers–Danlos syndrome (vEDS) who developed pneumothorax and was treated with a total pleural covering technique (TPC). A 24-year-old man developed repeat pneumothorax with intermittent hemo-sputum. Based on unusual radiological manifestations of lung lesions and physical findings, EDS was suspected as an underlying cause of the pneumothorax. Surgical treatment was performed using a mediastinal fat pad and TPC, and no relapse was seen up to 2 years after surgery. TPC is a less invasive surgical approach for selected patients with vEDS. Accurate underlying diagnosis of vEDS and systemic evaluation of vascular complications are necessary before planning surgery.

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Title: Total pleural covering technique for intractable pneumothorax in patient with Ehlers–Danlos syndrome
Authors: Yoshihisa Kadota
Eriko Fukui
Naoto Kitahara
Eiji Okura
Mitsunori Ohta
Publication date: 01-07-2016
Publisher: Springer Japan
Published in: General Thoracic and Cardiovascular Surgery / Issue 7/2016
Print ISSN: 1863-6705
Electronic ISSN: 1863-6713
DOI: https://doi.org/10.1007/s11748-014-0504-9

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Total pleural covering technique for intractable pneumothorax in patient with Ehlers–Danlos syndrome

Abstract

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Abstract

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